中国进行性脊肌萎缩PMA患者的神经心

PLoSOne.Jun4;10(6):e.doi:10./journal.pone..

NeuropsychologicalInvestigationinChinesePatientswithProgressiveMuscularAtrophy.

CuiB1,CuiL2,LiuM1,LiX1,MaJ1,FangJ1,DingQ1.

Authorinformation

1DepartmentofNeurology,PekingUnionMedicalCollegeHospital,ChineseAcademyofMedicalSciences,Beijing,China.

2DepartmentofNeurology,PekingUnionMedicalCollegeHospital,ChineseAcademyofMedicalSciences,Beijing,China;NeurosciencesCenter,ChineseAcademyofMedicalSciences,Beijing,China.

Abstract

BACKGROUND:

Progressivemuscularatrophy(PMA)isararetypeofdegenerativemotorneurondisease(MND)ofwhichtheonsethappensinadultperiod.Despiteitswell-definedclinicalcharacteristics,itsneuropsychologicalprofilehasremainedpoorlyunderstood,consideringtheconsensusofcognitiveandbehavioralimpairmentreachedinamyotrophiclateralsclerosis(ALS).

METHODS:

Weconductedacross-sectionalevaluationofChinesePMApatientswithaseriesof







































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