中国进行性脊肌萎缩PMA患者的神经心
PLoSOne.Jun4;10(6):e.doi:10./journal.pone..
NeuropsychologicalInvestigationinChinesePatientswithProgressiveMuscularAtrophy.
CuiB1,CuiL2,LiuM1,LiX1,MaJ1,FangJ1,DingQ1.
Authorinformation
1DepartmentofNeurology,PekingUnionMedicalCollegeHospital,ChineseAcademyofMedicalSciences,Beijing,China.
2DepartmentofNeurology,PekingUnionMedicalCollegeHospital,ChineseAcademyofMedicalSciences,Beijing,China;NeurosciencesCenter,ChineseAcademyofMedicalSciences,Beijing,China.
Abstract
BACKGROUND:
Progressivemuscularatrophy(PMA)isararetypeofdegenerativemotorneurondisease(MND)ofwhichtheonsethappensinadultperiod.Despiteitswell-definedclinicalcharacteristics,itsneuropsychologicalprofilehasremainedpoorlyunderstood,consideringtheconsensusofcognitiveandbehavioralimpairmentreachedinamyotrophiclateralsclerosis(ALS).
METHODS:
Weconductedacross-sectionalevaluationofChinesePMApatientswithaseriesof哪儿治疗白癜风好有什么药可以治白癜风